Dr.Archana Gunabalan
Dr.Ravali Yenepalli
Abstract
INTRODUCTION:RETINITIS PIGMENTOSA IS A RETINAL DEGENERATIVE CONDITION AFFECTING PHOTORECEPTORS. PREDOMINANTLY RODS ARE AFFECTED AND THEN LATER DEGENERATION OF CONES OCCURS.
CASE DESCRIPTION:A 45 YEAR OLD FEMALE PRESENTED WITH THE COMPLAINTS OF BLURRING OF VISION IN BOTH EYES FOR 1 YEAR.SHE ALSO HAD NIGHT BLINDNESS SINCE CHILDHOOD.SHE HAD DECOMPENSATED LIVER DISEASE.HER VISUAL ACUITY WAS CF@3M WITH PINHOLE 6/60 IN RIGHT EYE AND CF@2M WITH NO PINHOLE IMPROVEMENT.HER ANTERIOR SEGEMENT WAS NORMAL.FUNDUS EXAMINATION REVEALED THE CLASSIC TRIAD OF RETINITIS PIGMENTOSA.SHE ALSO HAD MACULAR HOLE IN HER LEFT EYE.
DISCUSSION: USUALLY MACULAR ABNORMALITIES SUCH AS EPIRETINAL MEMBRANE,CYSTOID MACULAR ODEMA,VITREOMACULAR TRACTION ARE SEEN IN PEOPLE WITH RETINITIS PIGMENTOSA.MACULAR HOLE IS A LESS FREQUENT COMPLICATION.


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